Surg Cosmet Dermatol. 2026;18(1):1-5
Bednar tumor is a rare variant of dermatofibrosarcoma protuberans. A 45-year-old woman presented with a progressively enlarging bluish macule on the shoulder. Biopsy revealed a pigmented spindle cell neoplasm, with immunohistochemistry positive for CD34 and negative for S100 and SOX-10. Surgical excision with margin mapping was performed. Surgical treatment with margin control is the gold standard for the management of Bednar tumor. This technique ensures complete resection, with outcomes comparable to those of Mohs micrographic surgery. This case highlights the importance of clinical suspicion in atypical hyperpigmented skin lesions.
Keywords: Dermatofibrosarcoma; Immunohistochemistry; Dermatology